Background: Agenesis of the inferior vena cava (IVC) is an extremely rare congenital malformation. Although frequently symptomatic, due to its low prevalence, agenesis of IVC may often be missed in the normal workup. Most of the reports are related to the loss of IVC alone, while the reports of simultaneous loss of IVC and bilateral iliac veins are rare. Acute deep venous thrombosis is also one of the causes of chronic deep venous ulcer, especially in children with acute deep venous thrombosis, which is an important cause of neglect and missed diagnosis. When color Doppler ultrasound cannot be clear, attention must be paid to computerized tomography examination.
Case Presentation: We reported a case of IVC below renal vein hypoplasia in an 8-year-old girl who presented bilaterally with persistent pain in both lower limbs. Ultrasonography revealed no clear IVC and iliofemoral venous system under the renal venous plane.
Conclusion: This case is a rare congenital malformation of IVC. It is rare in children with venous thrombosis-related symptoms. We intended to demonstrate the etiology of the appearance of venous thrombosis in children through this case.
Julie Jaffray , Guy Young Deep vein thrombosis in pediatric patients. Pediatr Blood Cancer.2018;65(3):e26881
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